Pseudo-Chediak-Higashi anomaly in a child with a hepatic vascular malformation.

Aún no traducido Aún no traducido
Autores
Categoría Estudio primario
RevistaThe American journal of pediatric hematology/oncology
Año 1986
A case of a congenital hepatic vascular malformation in a child complicated by disseminated intravascular coagulation and hemolytic anemia is presented. Examination of the peripheral blood disclosed the presence in the leukocytes of giant intracytoplasmic inclusions resembling those of the Chediak-Higashi anomaly. Ultrastructural analysis characterized those inclusions as phagocytosed red cell debris, a result of mechanical destruction of the red cells.
Epistemonikos ID: cb8fc490f12a0a9ceaa2351726ed2262cf4fc345
First added on: Dec 10, 2021